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Cell manganese-rescue experiments in the same paper must not be recast as manganese treatment of the patients.","comparator":null,"unit":null,"notes":"","entity":null},{"dimension":"nutrient_topic","value_text":"Manganese research collection; topical membership is not evidence of a direct dietary effect.","comparator":null,"unit":null,"notes":"","entity":{"slug":"manganese","display_name":"Manganese","entity_type_key":"nutrient_element"}},{"dimension":"organism","value_text":"Homo sapiens","comparator":null,"unit":null,"notes":"","entity":null},{"dimension":"plain_language","value_text":"Galactose improved selected blood sugar-chain markers despite the genetic defect.","comparator":null,"unit":null,"notes":"","entity":null},{"dimension":"primary_references","value_text":"[mn-clin-tmem165patients] Galactose Supplementation in Patients With TMEM165-CDG Rescues the Glycosylation Defects. 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Cell manganese-rescue experiments in the same paper must not be recast as manganese treatment of the patients.\nexposure: Oral D-galactose; indexed abstract reports 1 g/kg/day in individuals homozygous for c.792+182G>A.\ncross_nutrient: Human TMEM165 deficiency (underlying_defect)\nevidence_span: {\"source_cache\": \"artifacts/manganese-clinical-sources/tmem165patients.abstract.txt\", \"locator\": \"Indexed primary abstract\", \"file_sha256\": \"3899c8a8d58b702858b7e1e74723d46a9825f4d7846b969ccf33db688fa16eac\", \"start_char\": 0, \"end_char\": 2039, \"text_sha256\": \"3899c8a8d58b702858b7e1e74723d46a9825f4d7846b969ccf33db688fa16eac\", \"text_characters\": 2039}\n[mn-clin-tmem165patients] Galactose Supplementation in Patients With TMEM165-CDG Rescues the Glycosylation Defects. 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